SAQ 326 – Haematology – haemophilia A with ankle haemarthrosis

A 7-year-old boy with known haemophilia A presents after twisting his ankle while playing. The ankle is painful and swollen. He weighs 30 kg.

Define haemophilia A.

(Marked out of 1.0)

/ 1

Classify haemophilia A severity by residual factor VIII activity.

(Marked out of 3.0)

Severity	Residual factor VIII activity
Mild
Moderate
Severe

/ 3

State the most likely diagnosis for the ankle swelling.

(Marked out of 1.0)

/ 1

List two (2) supportive treatment measures.

(Marked out of 2.0)

/ 2

Specify the factor replacement, target activity, and approximate dose for this ankle presentation.

(Marked out of 3.0)

/ 3

If he had an intracranial haemorrhage, what factor VIII target and dose would be required?

(Marked out of 2.0)

/ 2

Total Score: 0 / 12

Percentage: 0%